Chinese Journal of Dermatology ›› 2024, Vol. 57 ›› Issue (10): 873-886.doi: 10.35541/cjd.20240222

• Guidelines and Consensus • Previous Articles     Next Articles

Guidelines for diagnosis and treatment of pemphigus in China (2024)

China Dermatologist Association; Treatment Group, Chinese Society of Dermatology; Dermatology Branch of China International Exchange and Promotive Association for Medical and Health Care; National Clinical Research Center for Dermatologic and Immunologic Diseases; Rare Skin Diseases Committee, China Alliance for Rare Diseases   

  1. China Dermatologist Association; Treatment Group, Chinese Society of Dermatology; Dermatology Branch of China International Exchange and Promotive Association for Medical and Health Care; National Clinical Research Center for Dermatologic and Immunologic Diseases; Rare Skin Diseases Committee, China Alliance for Rare Diseases
  • Received:2024-04-25 Revised:2024-07-23 Online:2024-10-15 Published:2024-09-29
  • Contact: Jin Hongzhong; Wang Gang E-mail:jinhongzhong@263.net; xjwgang@fmmu.edu.cn
  • Supported by:
    National High Level Hospital Clinical Research Funding (2022-PUMCH-B-092); National Key R&D Program of China (2022YFC3601800); Beijing Natural Science Foundation (7242109); National Key Clinical Specialty Project of China

Abstract: 【Abstract】 Pemphigus is a group of rare and severe autoimmune bullous diseases characterized by blisters, bullae, and erosions on the skin and/or mucous membranes. With the deep understanding of pemphigus and continuous update of treatment methods, it is necessary to formulate guidelines for the diagnosis and treatment of pemphigus in China. Hence, a guideline working group was established by relevant academic organizations. Based on available evidence in China and other countries, as well as China's national conditions, 12 clinical issues that need to be urgently solved were proposed and 30 recommendations were formulated on the diagnosis and treatment of pemphigus after multiple rounds of demonstration and selection, aiming to provide a reference for the diagnosis and treatment of pemphigus and to guide clinical practice.

Key words: Pemphigus, Diagnosis, Treatment, Glucocorticoids, Rituximab, Immunosuppressive agents, Guideline