中华皮肤科杂志 ›› 2014, Vol. 47 ›› Issue (11): 812-814.

• 研究报道 • 上一篇    下一篇

Parkes-Weber综合征伴假性Kaposi肉瘤一例

唐金玲1,树叶1,陈卫坚1,罗勇奇1,汤建萍2   

  1. 1. 湖南省儿童医院
    2. 长沙市湖南省儿童医院皮肤性病科
  • 收稿日期:2013-12-02 修回日期:2014-05-10 出版日期:2014-11-15 发布日期:2014-11-01
  • 通讯作者: 汤建萍 E-mail:jpingtang@126.com

A case of Parkes-Weber syndrome accompanied by pseudo-Kaposi′s sarcoma

  1. 1.
    2. Hunan Children's Hospital
  • Received:2013-12-02 Revised:2014-05-10 Online:2014-11-15 Published:2014-11-01

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摘要： 患者女，8岁7个月。右臀部紫红色斑8年，右下肢较左下肢逐渐增大7年余，多发性赘生物1年。皮肤科检查：右下肢较左下肢肥大且长，皮肤鲜红斑痣，皮温增高及皮肤大量赘生物伴有恶臭。X线、磁共振成像、多普勒超声提示高流速脉管畸形。皮肤病理可见血管增生，成纤维细胞增生及红细胞外溢，诊断为伴假性Kaposi肉瘤的Parkes-Weber综合征。

关键词: Parkes-Weber综合征, 假性Kaposi肉瘤, 动静脉瘘

Abstract: Tang Jinling, Shu Ye, Chen Weijian, Luo Yongqi, Tang Jianping. Department of Dermatology, Hunan Children′s Hospital, Changsha 410007, China Corresponding author: Tang Jianping, Email: jpingtang@hotmail.com 【Abstract】 A girl who aged eight years and seven months presented with prunosus patches on the right buttock for 8 years, gradual unilateral enlargement of the right lower limb for more than 7 years, and multiple vegetations for 1 year． Dermatological examination showed nevus flammeus and multiple malodorous vegetations over the right lower limb with high skin temperature. The right lower limb was thicker and longer than the left lower limb. X-ray examination, magnetic resonance imaging and Doppler ultrasound examination revealed high-flow vascular malformations. Pathological examination of the vegetations showed vascular proliferation, fibroblast proliferation and erythrocyte extravasation. She was diagnosed as Parkes-Weber syndrome accompanied by pseudo-Kaposi′s sarcoma.

Key words: Parkes-Weber syndrome, Pseudo-Kaposi′s sarcoma, Arteriovenous fistula

中图分类号: 

  • R751