遗传性血管性水肿诊疗路径皮肤科专家共识（2025版）

doi:10.35541/cjd.20240676

Abstract

Abstract: 【Abstract】 Hereditary angioedema （HAE） is a rare autosomal dominant hereditary disorder mediated by bradykinin and characterized by recurrent skin and/or mucosal edema. HAE attacks commonly affect the skin, upper respiratory tract and gastrointestinal tract. Laryngeal edema in HAE patients carries a high mortality rate. Enhancing dermatologists′ ability to diagnose and treat HAE can significantly improve patient outcomes. This consensus was developed based on Chinese and international high-quality literature in recent years and clinical experience of 19 dermatological experts in China, aiming to provide standardized diagnosis and treatment pathway for HAE.

Key words: Angioedemas, hereditary, Critical pathways, Dermatology, Consensus

Chinese Society of Dermatology, China Dermatologist Association. Recommendations for the diagnosis and treatment pathway for hereditary angioedema:a dermatology expert group consensus （2025 edition）[J]. Chinese Journal of Dermatology, 2025, 58(6): 497-502.doi:10.35541/cjd.20240676

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Recommendations for the diagnosis and treatment pathway for hereditary angioedema:a dermatology expert group consensus （2025 edition）

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