Abstract: 【Abstract】 A 9-year-old girl presented with a symptomless irregular dark brown papule on the vulva for 2 weeks. The patient was initially clinically diagnosed with pigmented nevus, and underwent surgical excision. Postoperative histopathological examination showed dilated glands and tubules in the dermis, eosinophilic secretions and pigment granules in the tubules, decapitation secretion in the inner layer cells, and flat myoepithelial cells around the tubules; a large amount of brown-black pigments were seen in the glands, tubular epithelium and interstitium, and lymphocytes and plasma cells infiltrated the interstitium. Finally, the diagnosis of pigmented apocrine hamartoma was made.

Key words: Apocrine hamartoma, Pigmented apocrine hamartoma, Apocrine tumor, Hamartoma