关键词: 乳糜反流综合征, 阴道漏, 乳糜, 淋巴管扩张

Abstract: Chen Aiming, Yu Shanshan, Zhang Wei. Department of Dermatology, First Affiliated Hospital of Soochow University, Suzhou 215006, China 【Abstract】 An 18-year-old woman was admitted to the hospital for swelling of the right lower limb and vulva with milky-white vesicles for 3 years. Skin examination revealed swollen and enlarged right lower limb and labium, numerous clustered or scattered pinhead- to millet-sized whitish thick-walled vesicles over the right labium majus, bilateral labium minus, vaginal orifice, and right thigh, with milky-white chylous fluid draining from the vagina. Magnetic resonance imaging revealed obvious lymphangiectasia in the lower abdominal cavity and right side of the pelvis, dilation and distortion of lymphatic vessels in the skin and subcutaneous tissue of the right inner thigh, the vaginal wall and at the medial side of the right labium majus, but no abnormality in the uterus. Histopathological examination of the milky-white vesicles showed cystic dilation of lymphatic vessels in the superficial dermis, and fibrous hyperplasia of the middle and lower dermis. A diagnosis of primary chylous reflux syndromeⅠ was made.

Key words: Chylous reflux syndrome, Vaginal fistula, Chyle, Lymphangiectasis