Abstract: 【Abstract】 Vascular tumors are relatively common in childhood and are usually benign. However, some vascular tumors may represent cutaneous manifestations of associated syndromes and can be accompanied by various complications. This review summarizes common syndromes associated with vascular tumors in children, including PHACE syndrome, LUMBAR syndrome, multiple infantile hemangiomas with hepatic hemangiomas, Kasabach?Merritt phenomenon, and Maffucci syndrome, with a focus on their clinical features and recent advances in diagnosis and treatment. The aim is to facilitate early clinical recognition, promote timely and appropriate management, and ultimately prevent disease progression.

Key words: Vascular tumors, PHACE syndrome, LUMBAR syndrome, Multifocal cutaneous infantile hemangiomas related hepatic hemangioma, Kasabach-Merritt phenomenon, Maffucci syndrome