皮疹伴发热、贫血为表现的VEXAS综合征1例

doi:10.35541/cjd.20220676

Chinese Journal of Dermatology ›› 2025, e20220676.doi: 10.35541/cjd.20220676

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A case of VEXAS syndrome presented with skin lesions, fever and anemia

Liu Ziqi¹, Lin Jinran¹, Wang Qian², Chen Lianjun¹, Chen Huyan¹, Le Yan¹, Zhang Yue¹, Wang Zhenhua², Zhu Ping², Ding Tianling², Huang Qiong¹

¹Department of Dermatology, Huashan hospital, Fudan University, Shanghai 200032, China; ²Department of Hematology, Huashan hospital, Fudan University, Shanghai 200032, China

Received:2022-09-21 Revised:2024-04-11 Online:2025-01-10 Published:2025-09-22
Contact: Huang Qiong E-mail:blueqiong1972@163.com
Supported by:
Shanghai Sailing Program（21YF1404400）

Abstract

Liu Ziqi, Lin Jinran, Wang Qian, Chen Lianjun, Chen Huyan, Le Yan, Zhang Yue, Wang Zhenhua, Zhu Ping, Ding Tianling, Huang Qiong. A case of VEXAS syndrome presented with skin lesions, fever and anemia[J]. Chinese Journal of Dermatology,2025,e20220676. doi:10.35541/cjd.20220676

References ［8］

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［7］	Alegría⁃Landa V, Rodríguez⁃Pinilla SM, Santos⁃Briz A, et al. Clinicopathologic, immunohistochemical, and molecular features of histiocytoid sweet syndrome［J］. JAMA Dermatol, 2017,153（7）:651⁃659. doi: 10.1001/jamadermatol.2016.6092.
［8］	Ferrada MA, Savic S, Cardona DO, et al. Translation of cytoplasmic UBA1 contributes to VEXAS syndrome pathogenesis［J］. Blood, 2022,140（13）:1496⁃1506. doi: 10.1182/blood.2022 016985.

A case of VEXAS syndrome presented with skin lesions, fever and anemia

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