中华皮肤科杂志 ›› 1993, Vol. 26 ›› Issue (2): 87-89.

• 论著 • 上一篇    下一篇

基底膜区TgA沉积大疱病20例分析

翁孟武, 邱丙森, 侯爱琴, 康克非   

  1. 上海医科大学皮肤病学研究所, 200040
  • 收稿日期:1991-12-12 修回日期:1992-05-12 出版日期:1993-04-15 发布日期:1993-04-15
  • 基金资助:
    卫生部基金资助课题

An analysis of 20 patients with IgA deposits at BMZ

WENG Meng-Wu, QIU Bing-Sen   

  1. Institede of Dermatology, Shanghai Medital Unversity, Shanghai 200040
  • Received:1991-12-12 Revised:1992-05-12 Online:1993-04-15 Published:1993-04-15

摘要: 20例基底膜区IgA沉积大疱病可分成3种,即成人线状IgA大疱病(LAD),成人线状IgA伴IgG大疱病(LAGD),儿童良性慢性大疱病(BGBDC).LAD中,大部分病人具有与疱疹样皮炎(DH)相似的病理学改变;而LAGD中,大部分病人具有与类天疱疮相似的病理学改变.上述两病伴口腔损害分别为43%和50%.大部分病人对氨苯砜(DDS)和雷公藤治疗有效.相反,BCBDC对DDS反应差.

关键词: 皮肤病,大疱性, IgA沉积

Abstract: A study of 20 patients with IgA deposits at BMZ sows that three conditions can he described: (1) Linear IgA bullous disease in adults (LAD), 7 cases; (2) Linear IgA and InG bullous disease in adults (LAGD), 10 cases; (3) Beaign chronic bullous dermatosis of childhood (BCBDC), 3 cases.

Key words: Skin diseases bullous, IgA deposits